Case Report on Failed Kasai Hepatico Portoenterostomy with Biliary Atresia in 3 years old child
Keywords:
Biliary Atresia, Bile duct, MRCP, Cholangiogram, Doppler study, Discharge drugs.Abstract
Biliary atresia is a rare liver disease in children where the bile ducts are blocked or not present in the liver. This case explains a 3 years old child who was previously diagnosed with Biliary Atresia. The Child admitted electively for cholangiogram and asses the possibility of interventional radiology guided Percutaneous transhepatic biliary Drainage insertion for biliary strictures. The child liver enzymes are increased and patient histopathology studies Indicates biliary atresia. The Child was diagnosed with Biliary atresia. Doppler study showed decreased peribiliary echogenicity, short segments of Centre prominent intrahepatic biliary radicals with intervening on dilated duct noted presented intrahepatic strictures. MRCP showed multifocal intrahepatic strictures, cystic dilation central part segment 3 intrahepatic biliary radicals positive. The patient underwent cholangiogram. Medications Used in the Course of Hospitalization are Prograf 1mg and 0.5mg, Mycophenolate Mofetil 250-125mg, Omnacortil 2.5mg and Sirolimus 1mg. Child was hemodynamically stable, vitals are normal, accepting feed well and discharge. Discharge medications are Sirolimus 1mg, Prograf 0.5mg, Ciplox 125mg, Omnacortil 2.5mg, Udcament 2.5ml, Cellcept 250mg.
Downloads
References
Sundaram SS, Mack CL, Feldman AG, Sokol RJ. "Biliary Atresia: Indications and Timing of Liver Transplantation." Seminars in Liver Disease. 2012;32(2):147-154. doi:10.1055/s-0032-1316484
Ng VL, Haber BH, Magee JC, et al. "Medical status of 219 children with biliary atresia surviving long-term with their native livers: results from a North American multicenter consortium." Journal of Pediatrics. 2014;165(3):539-546.e2.doi: 10.1016/j.jpeds.2014.04.064
Neuberger JM, et al."post-transplant immunosuppression and complications."Lancet. 2017;389(10084):1098– 1111.doi:10.1016/S0140-6736(16)32415-0
Ding Y, Zhou J, Xu Y, et al. "Efficacy and Safety of Sirolimus in Pediatric Liver Transplant Recipients: A Systematic Review and Meta-Analysis." Pediatric Transplantation. 2020;24(3):e13644. doi:10.1111/petr.13644
Bramall AN, Soo E, Ng VL. "Radiologic Management of Biliary Complications After Pediatric Liver Transplantation." Pediatric Radiology. 2018;48(1):47–58. doi:10.1007/s00247-017-3947-2
Iyer KR, et al. "Interventional radiology in pediatric liver transplantation: Indications and outcomes."
Journal of Pediatric Surgery. 2019;54(11):2302–2309. doi: 10.1016/j.jpedsurg.2019.05.034
Kim WR, Lake JR, Smith JM, et al. "OPTN/SRTR 2017 Annual Data Report: Liver." American Journal of Transplantation. 2019;19(Suppl 2):184–283. doi:10.1111/ajt.15200.
Downloads
Published
How to Cite
Issue
Section
License
This work is licensed under a Creative Commons Attribution 4.0 International License.
You are free to:
- Share — copy and redistribute the material in any medium or format
- Adapt — remix, transform, and build upon the material for any purpose, even commercially.
Terms:
- Attribution — You must give appropriate credit, provide a link to the license, and indicate if changes were made. You may do so in any reasonable manner, but not in any way that suggests the licensor endorses you or your use.
- No additional restrictions — You may not apply legal terms or technological measures that legally restrict others from doing anything the license permits.
