Descriptive Epidemiology of Anorectal Malformations in Chinese Population

Authors

  • Christoph Heinrich Houben The Chinese University of Hong Kong Prince of Wales Hospital Shatin, N.T. Hong Kong
  • Kin Wai Edwin Chan Prince of Wales Hospital Shatin, N.T. Hong Kong
  • Kit Yi Kristine Pang Prince of Wales Hospital Shatin, N.T. Hong Kong
  • Xiang-Nan Feng The Chinese University of Hong Kong Shatin, N.T. Hong Kong
  • Wai Cheung Jennifer Mou Prince of Wales Hospital Shatin, N.T. Hong Kong
  • Yuk Him Tam Prince of Wales Hospital Shatin, N.T. Hong Kong
  • Kim Hung Lee Prince of Wales Hospital Shatin, N.T. Hong Kong

DOI:

https://doi.org/10.21699/jns.v6i4.531

Keywords:

Anorectal malformation, Perineal fistula, Rectourethral fistula, VACTERL association, Down Syndrome, Krickenbeck classification

Abstract

Over a twelve year period one hundred and five neonates (30 females) with an anorectal malformation (ARM) were studied at a tertiary referral centre in Hong Kong. A perineal fistula was the most frequent presentation of ARM in males closely followed by rectourethral fistula. Vestibular fistula was the most common anomaly amongst females. An ARM without a fistula was documented in 11 % of patients and dominated by males. Associations and syndromes were present in nearly 30 % of the group with VACTERL association and Down syndrome at the forefront. Isolated anomalies were most frequently seen in the renal tract (23 %), the CNS (20 %) and the heart (18 %). A quarter of the cohort was small for gestational age with syndromes/associations featuring in half of this subgroup. A death rate of 9.5 % was recorded, of which all except one had an underlying syndrome or association. In addition a pre-existing heart condition constituted the most significant factor affecting the mortality in 50 % of this group.

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Author Biographies

Christoph Heinrich Houben, The Chinese University of Hong Kong Prince of Wales Hospital Shatin, N.T. Hong Kong

Department of Surgery, ass Professor

Kit Yi Kristine Pang, Prince of Wales Hospital Shatin, N.T. Hong Kong

Department of Surgery, ass Consultant

Xiang-Nan Feng, The Chinese University of Hong Kong Shatin, N.T. Hong Kong

Department of Statistics

Wai Cheung Jennifer Mou, Prince of Wales Hospital Shatin, N.T. Hong Kong

Department of Surgery, ass Consultant

Yuk Him Tam, Prince of Wales Hospital Shatin, N.T. Hong Kong

Department of Surgery, Consultant

Kim Hung Lee, Prince of Wales Hospital Shatin, N.T. Hong Kong

Department of Surgery, Consultant

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Published

2017-10-08

How to Cite

1.
Houben CH, Chan KWE, Pang KYK, Feng X-N, Mou WCJ, Tam YH, Lee KH. Descriptive Epidemiology of Anorectal Malformations in Chinese Population. J Neonatal Surg [Internet]. 2017Oct.8 [cited 2021Apr.16];6(4):74. Available from: https://jneonatalsurg.com/ojs/index.php/jns/article/view/403

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