Fetal Lung Interstitial Tumor (FLIT): A case series

Kah Ann Ho; Noemi A Fuentes-Bolanos; Andrew J Gifford; Ashish Jiwane; Dylan Wanaguru

doi:10.47338/jns.v12.1141

Authors

Kah Ann Ho The Toby Bowring Department of Paediatric Surgery, Sydney Children’s Hospital, Randwick NSW, Australia; School of Clinical Medicine, Faculty of Medicine and Health, UNSW, Sydney NSW, Australia https://orcid.org/0000-0002-5206-6154
Noemi A Fuentes-Bolanos Children’s Cancer Institute, Lowy Cancer Centre, UNSW Sydney, Sydney, NSW, Australia; Kids Cancer Centre, Sydney Children’s Hospital, High Street, Randwick, Sydney, NSW, Australia; School of Women and Children’s Health, Faculty of Medicine, UNSW Australia, Sydney, NSW, Australia https://orcid.org/0000-0001-6880-5428
Andrew J Gifford Anatomical Pathology, NSW Heath Pathology, Prince of Wales Hospital, Randwick, New South Wales, Australia; School of Clinical Medicine, UNSW Medicine & Health, UNSW Sydney, Sydney, NSW, Australia
Ashish Jiwane The Toby Bowring Department of Paediatric Surgery, Sydney Children’s Hospital, Randwick NSW, Australia; School of Women and Children’s Health, Faculty of Medicine, UNSW, Randwick NSW, Australia
Dylan Wanaguru The Toby Bowring Department of Paediatric Surgery, Sydney Children’s Hospital, Randwick NSW, Australia; School of Women and Children’s Health, Faculty of Medicine, UNSW, Randwick NSW, Australia

DOI:

https://doi.org/10.47338/jns.v12.1141

Keywords:

Fetal lung interstitial tumor, Pediatric lung tumor, Fetal lung mass, Neonatal tumor, Case report

Abstract

Background: Fetal Lung Interstitial Tumor (FLIT) is a rare benign lung tumor. There have been 18 cases of FLIT described in the literature. FLIT is characterized by a region of arrested lung development and must be differentiated from other congenital lung lesions with poorer prognoses.

Case Presentation: We report the first two known cases of FLIT in Australia and New Zealand. In both cases, the patients developed respiratory distress at birth requiring intubation. Imaging revealed solid lesions and echocardiography demonstrated pulmonary hypertension. The patients underwent surgical resection without any complications or recurrence.

Conclusion: FLIT is a rare benign congenital lung tumor that can be adequately managed with surgical resection.

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